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La L-Carnitina se une a ellos y forma un complejo que atraviesa la membrana mitocondrial interna gracias a la accin de la enzima carnitina palmitoiltransferasa I (CPT-I)

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Lithium's effects on cyclic AMP, membrane transport and cholinergic mechanisms

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Angelini C, Trevisan C, Isaya G, Pegolo G, Vergani L: Clinical varieties of carnitine and carnitine palmitoyltransferase deficiency

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The peripheral neuropathy in Fabry disease is described as a small fibre neuropathy, meaning that small, unmyelinated nerve fibres are particularly affected [82]

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Significance of L-Carnitine for Human Health 4-Daniel W Foster Ann N Y Acad Sci

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