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Progress in brain research

Affected people should eat a high-carbohydrate, low-fat diet and avoid fasting

1 ml cada 3,4 kg bloquea hasta T5

: L-Carnitine : ,

Para ello se une a la molcula del cido graso activado (acil-CoA), generando acilcarnitina, y a travs de una enzima transportadora de la membrana mitocondrial interna permite el paso de esta molcula al interior mitocondrial, donde se separa de nuevo para que el cido graso contine la ruta y se obtenga adenosn trifosfato (ATP)